Pirker, W.W.PirkerBack, C.C.BackGerschlager, W.W.GerschlagerLaccone, Franco A.Franco A.LacconeAlesch, F.F.Alesch2018-11-072018-11-072003https://resolver.sub.uni-goettingen.de/purl?gro-2/46529We report on a patient with spinocerebellar ataxia type 2 (SCA 2) with an unusual clinical presentation, including severe, disabling resting and action tremor and the successful treatment of this tremor syndrome with chronic thalamic stimulation. Using [I-123]beta-CIT single photon emission computed tomography, we document a marked degeneration of the nigrostriatal dopaminergic system in SCA 2. (C) 2002 Movement Disorder Society.journal_article10.1002/mds.10192000181007900018